Among the 80 cases of odontogenic myxomas diagnosed at their service unit, 10 12. A gelatinous tumor can be seen attached by a narrow pedicle to the atrial septum. Odontogenic fibroma pdf odontogenic fibroma pdf odontogenic fibroma pdf download. Morgan odontogenic tumors comprise a range of disorders of growth, from malignant and benign. Myxoma is a rare, benign stromal tumor of mesenchymal origin often confused with other conjunctival stromal tumors.
Click on the link above to view the information page. It is nonencapsulated, arises from odontogenic ectomesenchyme, develops solely in the jaws, and represent a small percentage of odontogenic tumor overall. Of all the biopsies submitted, odontogenic tumors comprise about 1. Odontogenic myxoma gupta s, grover n, kadam a, gupta s. Odontogenic fibroma pdf the odontogenic fibroma is a rare, object oriented systems development ali bahrami free pdf dow benign tumor of mesodermal origin, and one of the most illdefined and least understood of all odontogenic neoplasms. Odontogenic myxoma is a rare tumour of the jaw, making both its diagnosis and management challenging.
A case of a rapidly expanding odontogenic myxoma of the mandible. Epidemiology typically seen in the 2nd to 3rd decades of life slightly earlier than ameloblastomas. Odontogenic myxoma is a rare and locally invasive benign neoplasm found exclusively in jaws. Odontogenic tumors at university of colorado health. It is believed to arise from odontogenic ectomesenchyme and consists of rounded and angular cells embedded in abundant mucoid stroma. Odontogenic myxoma of the mandible ramya sree s1, vardendra g kulkarni2, chandrashekhar hr3, shivamurthy kc4 abstract. Odontogenic myxoma in an adolescent patient report of a. The lack of tooth vitality is not supportive of an odontogenic myxoma. The age of the patient, the expansion and perforation of bone are all in support of the behavior of a neoplasm including a neoplasm of tooth origin such as an odontogenic myxoma.
The second and third decades of life are mostly affected and most studies report a. May 29, 2014 educational video created by unmc college of dentistry class of 2016 dental students. Treatment, symptoms, causes, complications, diagnosis. Research article characteristic features of the odontogenic myxoma on cone beam computed tomography 1kaili wang, 1wenhao guo, 2meng you, 2li liu, 2bei tang and 2guangning zheng 1state key laboratory of oral diseases, sichuan university, chengdu, china. What links here related changes upload file special pages permanent link page. Clinical examination revealed a diffuse swelling, measuring about 2. When the lesion is large and when presenting in a difficult location, aggressive initial therapy affords the most successful outcome. It represents approximately 3 6% of all odontogenic tumors. Surgical management of an uncommon cutaneous myxoma. Despite the benign nature of this lesion, there is a high. It is thought to arise from mesenchymal origin with cells of microscopic similarity to dental pulp and follicle 3. We present an unusual case of om as a rapidly expanding lesion in the mandible of a 62yearold woman who. Majority of myxomas that occur are present on the left side of the heart.
It can occur at any age but most commonly in the second and third decades of life. The aim of this paper is to report a case of odontogenic myxoma that affected the right maxilla and maxillary sinus. Odontogenic myxoma is a rare benign tumor unencapsulated aggressive and located character, originating from mesenchymal cells. Odontogenic myxoma is a rare, benign, locally aggressive and non metastasizing neoplasm which is believed to arise from the odontogenic ectomesenchyme and bears a close microscopic resemblance to mesenchymal portion of a tooth germ. It is not common among the youth below the age of 16. Odontogenic myxoma om is a locally invasive neoplasm unique to the tooth bearing areas of the jaw bones. A collection of disease information resources and questions answered by our genetic and rare diseases information specialists for odontogenic myxoma. More common in mandible than maxilla 23 in mandible clinical features. Maxillary odontogenic myxoma involving the maxillary sinus.
Most cases diagnosed in 2nd 4th decades but wide age range of occurrence between 1 to 73 years more common in women sites. Odontogenic myxoma is a rare lesion, with characteristics that are similar to those of other oral lesions, and this requires knowledge on the lesion, a detailed exam and histopathology in order to establish an early diagnosis and to offer a safe and riskfree treatment to the patient, avoiding sequelae and extensive mutilations which are common. Below are the links to the authors original submitted files for images. Odontogenic myxomas of the maxillofacial region are benign lesions, without preference for gender, race or location, with extremely varied clinical and. The evidence for its odontogenic origin arises from its almost exclusive location in the toothbearing areas of the jaws, its occasional association with missing or unerupted teeth and the presence of. The myxoma has an irregular surface and nearly fills the left atrium. The childrens hospital boston has an information page on odontogenic tumors in general. Odontogenic myxoma is a benign odontogenic tumor with locally aggressive behavior, and is relatively rare in the oral cavity. Odontogenic myxoma of the maxilla a rare case report ramkumar subramaiam, 1 sangeetha narashiman, 2 malathi narasimhan, 3 veda giri, 4 and santhosh kumar 5 1 professor, department of oral and maxillofacial surgery, faculty of dental sciences, sri ramachandra university, ramachandra nagar, porur chennai, tamilnadu, india. Odontogenic myxomas are rare tumors that involve the mandible or maxilla and account for 36% of odontogenic tumors 2. The odontogenic myxoma is an uncommon benign odontogenic tumor arising from embryonic. In the majority of cases, diagnosis is largely dependent on the histopathological findings.
Odontogenic myxoma om is a benign intraosseous neoplasia, not very frequent, 1 but with high infiltrative potential that makes it a locally invasive tumor. Odontogenic myxoma of the maxilla invading the maxillary sinus. Radiology radiolucency with septae histology spindlestellate fibroblasts with basophilic ground substance treatment en bloc resection. This study evaluated the literature concerning the surgical management of odontogenic myxoma, and reports the longterm outcome of a. Similar peak age of presentation can also have spindled cells but usually more cellular and fibrocollagenous with strands of odontogenic epithelium calcifications can be seen in the epithelium osteochondromyxoma. Conjunctival myxomas are thought to originate in tenons capsule and can masquerade as conjunctival lymphoma, lymphangioma, ocular surface squamous neoplasia ossn, or amelanotic melanoma. Mar 19, 2012 the odontogenic myxoma is an uncommon benign odontogenic tumor arising from embryonic connective tissue associated with tooth formation. The odontogenic myxoma is a rare, benign tumor that does not shed metastasis and involves the maxillomandibular complex. These tumors are usually located on the atrial septum. Odontogenic myxoma om is a rare entity of slowly growing benign neoplasm of ectomesenchymal origin, comprising of 36% of all odontogenic tumors that. Pdf odontogenic myxoma of the mandible researchgate.
The odontogenic myxoma is a relatively rare benign tumor occurring in the jaws. Dance center head and neck tumor conference charles limb, md 61 yo caucasian female 1 year history of right posterior triangle neck mass, fluctuating in size sx occasional pain. This report describes a case of odontogenic myxoma producing diffusely dispersed calcified products in a pattern. Myxoma is mostly seen in adult or elderly animals and although there is no sex predilection, it is supposed that doberman pincher and german shepherd dogs have a racial predisposition 8. Myxomas are usually located in either the left or right atrium of. Nonetheless, odontogenic myxoma should be placed high on the differential diagnosis. Odontogenic myxoma invading the maxillary sinus case presentation case report introduction myxoma arising in the facial bones is a rare tumor. Radiographically it presents most often as a multiloculated radiolucency 2. Pdf odontogenic myxomas are benign but locally aggressive neoplasms found almost exclusively in the jaws and arise only occasionally in other bones.
Odontogenic myxoma segmental mandibulectomy stellate and spindleshaped cells immunohistochemical staining a b s t r a c t odontogenic myxoma om is a rare benign neoplasm with locally aggressive behavior. Odontogenic myxoma of maxilla in an atypical location. Odontogenic myxoma odontogenic myxofibroma odontogenic fibromyxoma epidemiology. Report of two cases sridhar p reddy 1, ananth naag 1, bina kashyap 2 1 department of oral and maxillofacial surgery, st joseph dental college and hospital, duggirala, eluru, andhra pradesh, india 2 department of oral pathology, st joseph dental college and hospital, duggirala, eluru, andhra pradesh, india. Odontogenic myxoma represents an uncommon benign neoplasm comprising of 36% of all odontogenic tumors. When the lesion is large and when presenting in a difficult location, aggressive. Peripheral odontogenic myxoma is a rare odontogenic tumor representing an extra osseous counterpart of central odontogenic myxoma. Rare tumor of the jaw, odontogenic myxomafibromyxoma. A case of a rapidly expanding odontogenic myxoma of the. Mar 14, 2016 odontogenic myxoma is a benign odontogenic tumour of the jaw 1. Educational video created by unmc college of dentistry class of 2016 dental students. Odontogenic myxoma om is a rare benign neoplasm with locally aggressive behavior. Odontogenic myxoma is a benign locally aggressive neoplasm with a sparse prevalence and incertitude histogenesis. This tumour often presents as an asymptomatic expansile lesion without sensory nerve changes 2.
Odontogenic myxoma of the jaws is a rare slow growing, benign tumor of mesenchymal tissue origin and is characterized grossly by mucoid or gelatinous graywhitish tissue that replaces the cancellous bone and expands the cortex. Odontogenic myxomas are benign but locally aggressive neoplasms found almost exclusively in the jaws and arise only occasionally in other bones. Odontogenic myxoma is an uncommon benign mesenchymal odontogenic tumor arising from the dental papilla, follicle, or the periodontal ligament. Odontogenic myxoma a rare case and diagnostic and therapeutic challenges elitsa g. Odontogenic myxoma is a rare slow growing, benign, locally aggressive tumor of ectomesenchymal origin with or without odontogenic epithelium, comprising 3%. Odontogenic myxoma is a rare benign but locally aggressive odontogenic tumor. This is a case report of odontogenic myxoma in a 32 year old female patient and the treatment rendered to her. We present an unusual case of om as a rapidly expanding lesion in the mandible of a 62yearold woman who underwent segmental mandibulectomy and primary mandibular reconstruction using a titanium plate. If you have problems viewing pdf files, download the latest version of adobe reader. Usually present in a younger age group with the nasal cavity being the most common site. Odontogenic myxoma is a benign mesenchymal odontogenic tumor that is more frequently found in the mandibular molar region.
An irregular soft tissue mass lesion is seen arising from right maxillary bone alveolar process, measuring 6 x 4. It presents local invasiveness and tendency to recurrence. Odontogenic myxomas oms are benign tumors derived from embryonic mesenchymal elements of dental anlage. This study evaluated the literature concerning the surgical management of odontogenic myxoma, and reports the longterm outcome of a case managed. The patient had no documents pertaining to the previous treatment. There are currently no clear surgical management guidelines for odontogenic myxoma, and a variety of approaches may be used. Odontogenic myxoma is a benign odontogenic tumour of the jaw 1. Myxoma as stated is a tumor present near the heart. Odontogenic myxoma ddmfr oral and maxillofacial radiology. It has sheets and strands of odontogenic epithelial cells. Odontogenic myxoma is a rare slow growing, benign, locally aggressive tumor of ectomesenchymal origin with or without odontogenic epithelium, comprising 3% to 6% of all odontogenic tumors.
Similarity of protein profiles of extracellular matrix of dental follicle df of a. Odontogenic myxoma genetic and rare diseases information. It is commonly seen in gingiva between the 3rd and 4th decades of. Jan 30, 2019 myxoma as stated is a tumor present near the heart. Odontogenic myxoma normally affects people in their second and third decades of life. Deliverska, department of oral and maxillofacial surgery, faculty of dental medicine, medical university, sofia, bulgaria issn. This articles presents a rare case of odonogenic myxoma occurring in the mandible with a brief overlight on its etiology,immunocytohistochemistry,radilogical and treatment fetaures of odontogenic myxoma. Odontogenic myxoma definition of odontogenic myxoma by. Odontogenic myxoma originates from dental papilla or follicular mesenchyme slow growing, aggressively invasive multilocular, expansile. The odontogenic myxoma is an uncommon benign odontogenic tumor arising from embryonic connective tissue associated with tooth formation. This paper reports a 6year followup case of an odontogenic myxoma treated with wide resection and mandibular bone reconstruction for posterior rehabilitation with dental implants. Research article characteristic features of the odontogenic.
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